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A desmoid tumor, also known as aggressive fibromatosis, is a rare and locally aggressive type of soft tissue tumor. Unlike malignant tumors, desmoid tumors do not metastasize to distant organs, but they can invade surrounding tissues and organs, causing significant morbidity. These tumors typically arise from the connective tissue, often in the abdominal wall, but can occur in other areas such as the extremities and the chest. The exact cause of desmoid tumors is not well understood, and they can occur sporadically or in association with familial adenomatous polyposis (FAP), a hereditary condition. Desmoid tumors are characterized by the abnormal growth of fibrous tissue, leading to the formation of firm, rubbery masses. Although they are non-cancerous, their local invasiveness can pose challenges in terms of management and treatment. Diagnosis of desmoid tumors involves imaging studies such as CT scans, MRI, or ultrasound, along with a biopsy to confirm the nature of the tumor. Treatment approaches vary and may include surgery, radiation therapy, or a watch-and-wait strategy, depending on factors like tumor location, size, and symptoms. Recurrence is not uncommon, necessitating a multidisciplinary approach to address the complex nature of these tumors. Desmoid tumors can be physically and emotionally challenging for individuals affected by them. Supportive care, close monitoring, and collaboration between healthcare professionals are crucial elements in managing desmoid tumors and improving the quality of life for those impacted by this rare condition.
